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Abstract
Ohtahara syndrome is a rare epileptic encephalopathy in children which usually presents at early age, characterized by an abnormal EEG and intractable seizure. We reported a 18-day-old male infant with seizure frequency of 20 times a day. Physical examination showed normal vital sign and general condition. Neurological assessment revealed an increase of physiological reflexes. An electroencephalogram was performed and showed burst suppression pattern suggested Ohtahara syndrome. An abnormality was found in non-contrast brain CT scan. The patient was managed with antiseizure medication. Subsequently, the patient showed an improvement. This case report highlights the importance of early diagnosis, proper management, and prognosis of children with Ohtahara syndrome.
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References
- Panayiotopoulos, C. P. (2005). Epileptic Encephalopathies in Infancy and Early Childhood in Which the Epileptiform Abnormalities May Contribute to Progressive Dysfunction. In: Panayiotopoulos CP. The Epilepsies: Seizures, Syndromes and Management. Oxfordshire (UK): Bladon Medical Publishing. Available from: https://www.ncbi.nlm.nih.gov/books/NBK2611/
- Nieh, S. E., Sherr, E. H. (2014). Epileptic encephalopathies: New Genes and New Pathways. Neurother. 11:796-806 Khan, S., Baradie, RA. (2012). Epileptic Encephalopathies:
- An Overview. Epilepsy Res Treat. ;2012:403592.
- Panayiotopoulos, C. P. (2005). Neonatal Seizures and Neonatal Syndromes. In: Panayiotopoulos CP. The Epilepsies: Seizures, Syndromes and Management. Oxfordshire (UK): Bladon Medical Publishing. Available from:
- https://www.ncbi.nlm.nih.gov/books/NBK2599/
- Beal, J. C., Cherian, K., Moshe, S. L. (2012) Early-onset epileptic encephalopathies: Ohtahara syndrome and early myoclonic encephalopathy. Pediatr Neurol. 47(5):317-23.
- Moumen, A. E. 2023. Ohtahara Syndrome: Case Report and Literature Review. Sch J Med Case Rep.11(4): 594- 596.
References
Panayiotopoulos, C. P. (2005). Epileptic Encephalopathies in Infancy and Early Childhood in Which the Epileptiform Abnormalities May Contribute to Progressive Dysfunction. In: Panayiotopoulos CP. The Epilepsies: Seizures, Syndromes and Management. Oxfordshire (UK): Bladon Medical Publishing. Available from: https://www.ncbi.nlm.nih.gov/books/NBK2611/
Nieh, S. E., Sherr, E. H. (2014). Epileptic encephalopathies: New Genes and New Pathways. Neurother. 11:796-806 Khan, S., Baradie, RA. (2012). Epileptic Encephalopathies:
An Overview. Epilepsy Res Treat. ;2012:403592.
Panayiotopoulos, C. P. (2005). Neonatal Seizures and Neonatal Syndromes. In: Panayiotopoulos CP. The Epilepsies: Seizures, Syndromes and Management. Oxfordshire (UK): Bladon Medical Publishing. Available from:
https://www.ncbi.nlm.nih.gov/books/NBK2599/
Beal, J. C., Cherian, K., Moshe, S. L. (2012) Early-onset epileptic encephalopathies: Ohtahara syndrome and early myoclonic encephalopathy. Pediatr Neurol. 47(5):317-23.
Moumen, A. E. 2023. Ohtahara Syndrome: Case Report and Literature Review. Sch J Med Case Rep.11(4): 594- 596.